Osler-Weber-Rendu Syndrome

Conveniently located to serve the areas of Westlake, OH

Osler-Weber-Rendu Syndrome, also known as hereditary hemorrhagic telangiectasia (HHT), is a rare genetic disorder that affects the blood vessels throughout the body. It is characterized by abnormal blood vessels that can cause spontaneous, recurring nosebleeds (epistaxis), small, dilated blood vessels near the surface of the skin (telangiectasias), and AVMs: arteriovenous malformations – abnormal connections between arteries and veins. HHT is an autosomal dominant disorder, which means that it can be passed down from one generation to the next. (1)

Dr. David Naar at Westlake’s Premier Vein Clinic is a highly skilled vascular surgeon who specializes in treating venous diseases and disorders. During a personal consultation, Dr. Naar will evaluate your medical history, perform a physical examination, and discuss your symptoms and concerns. This comprehensive assessment allows Dr. Naar to develop an individualized treatment plan tailored to a patient’s specific needs and goals.

To schedule a personal consultation with Dr. Naar, call (440) 641-0433 or use our convenient online form.

About HHT

Research estimates that between 1.5 and 2 people in every 10,000 have HHT. (1) It is characterized by the development of abnormal blood vessels throughout the body. These abnormal blood vessels, called telangiectasias or spider veins, are microscopic dilations of the capillaries that often appear as small red or purple spots on the skin or mucous membranes. Resembling a spider web or branches of a tree, telangiectasias can occur on various parts of the body, including the face, legs, and ankles. While they are not dangerous or harmful to your health, they can be aesthetically displeasing and impact self-confidence. One study revealed that those with HHT suffered discomfort due to nosebleeds, anxiety, and depression because of their condition. (2)

Types of HHT

There are four types of HHT:

  • Type 1: This type is characterized by the presence of telangiectasias and AVMs in the liver, lungs, brain, and gastrointestinal tract.
  • Type 2: Type 2 HHT is distinguished by the presence of pulmonary arteriovenous malformations (PAVMs) without significant liver involvement.
  • Type 3: Type 3 HHT is associated with cerebral arteriovenous malformations (CAVMs) and may also present with mild skin discoloration.
  • Type 4: In Type 4 HHT, patients experience telangiectasias and AVMs in the lungs, but not in other organs.

HHT Symptoms

Many individuals with HHT have a family history of the disease, although some cases may arise spontaneously through new gene mutations without a family history. Symptoms may include:

  • Nosebleeds (epistaxis)
  • Telangiectasias
  • Arteriovenous Malformations (AVMs)
  • Gastrointestinal Bleeding
  • Iron Deficiency Anemia
  • Skin Discoloration
  • Liver Problems

Benefits of Sclerotherapy

Sclerotherapy is a medical procedure used to treat varicose veins, reticular veins, and telangiectasias/spider veins. It involves injecting an irritant solution directly into the affected veins, causing them to collapse and eventually fade away.

Its benefits include the following:

  • Minimally Invasive: Sclerotherapy is a non-surgical cosmetic treatment involving the injection of a sclerosing agent directly into the affected blood vessels. There are no incisions or extensive recovery periods associated with this minimally invasive approach.
  • Enhanced Aesthetics: By eradicating unsightly varicose veins or spider veins, individuals can enjoy improved blood vessel aesthetic enhancement and achieve smoother, clearer skin.
  • Customized Treatments: Our expert medical team carefully evaluates each patient’s unique condition, allowing us to tailor the treatment plan to their specific needs.
  • Short Procedure Duration: Most sclerotherapy sessions can be completed within 30 minutes to an hour, making them convenient for individuals with busy schedules.
  • Minimal Side Effects: Temporary side effects such as mild bruising, swelling, or discomfort at the injection site are common but generally resolve quickly.
  • Long-Lasting Results: Sclerotherapy typically provides long-term results after several treatment sessions, leading to improved self-confidence and enhanced quality of life.

Who is a Candidate for Sclerotherapy?

Sclerotherapy for telangiectasias is suitable for individuals who meet certain criteria as potential candidates. Ideal candidates include those who:

  • Desire an improvement in the appearance of visible veins on their legs or face.
  • Experience self-consciousness or emotional distress due to the presence of spider veins or broken capillaries.
  • Have good overall health and do not have any significant underlying medical conditions that could interfere with the healing process.
  • Are realistic about the outcome of the treatment and have reasonable expectations.
  • Are committed to following post-treatment guidelines provided by Dr. Naar.

Personal Consultation

During your initial consultation with Dr. David Naar, he will conduct a detailed examination of the affected areas to assess the severity of your telangiectasias and ensure sclerotherapy is the right treatment for you. Additionally, Dr. Naar will review your medical history and inquire about any current medications or previous vein treatments. This information helps our medical team tailor the procedure to your individual needs and achieve optimal results. We encourage open communication during the consultation, as it allows us to address any concerns or questions you may have.

To schedule a personal consultation at Premier Vein Clinic with Dr. Naar, please contact our office at (440) 641-0433.

Preparation

Preparing for your sclerotherapy procedure is essential to maximize its effectiveness and minimize potential risks. Before your treatment, we will provide you with comprehensive preoperative instructions designed to optimize your safety and recovery. Follow these instructions diligently to ensure the best possible outcome:

  • Discontinue the use of blood thinners, supplements, and medications that may interfere with blood clotting, as instructed by your healthcare provider.
  • Inform us of any chronic health conditions, allergies, or skin conditions you may have.
  • Avoid prolonged exposure to direct sunlight or artificial tanning methods leading up to your procedure.
  • Wear loose-fitting clothing on the day of treatment to ensure comfort and allow easy access to the injection sites.
  • You will be able to drive.

Sclerotherapy Procedure

Sclerotherapy for telangiectasias is typically performed on an outpatient basis, meaning you can return home shortly after the procedure concludes. Before the procedure, Dr. Naar will clean and sterilize the targeted area. He will then inject a special sclerosing agent directly into the affected blood vessels using a fine needle. The sclerosing agent will cause irritation and inflammation within the treated veins. This prompts the buildup of scar tissue, ultimately collapsing and closing off the vein

Dr. Naar may apply pressure to the treated area to encourage optimal contact between the medication and the vein walls. Depending on the size and number of veins being treated, additional injections may be necessary to ensure all desired areas are addressed. After the injections are complete, Dr. Naar will cover the treatment area with a sterile dressing or compression garments to aid in healing and prevent blood from re-entering the treated vessels.

Will I need Anesthesia for Sclerotherapy?

Sclerotherapy for telangiectasias is typically performed without the need for anesthesia, as the injections themselves are generally well-tolerated by most patients. The sclerosing agent used during the procedure has a numbing effect on the surrounding tissue, minimizing any discomfort experienced. However, patients with heightened sensitivity or anxiety may request a local anesthetic cream before treatment to further reduce any potential discomfort.

Recovery

Following your sclerotherapy procedure, it is essential to follow post-treatment guidelines provided by your medical provider to ensure optimal healing and successful outcomes. Engaging in light physical activity, such as walking, can improve circulation and prevent blood clots. Wearing compression stockings or bandages after sclerotherapy can help reduce swelling, promote healing, and provide support to the treated veins. Dr. Naar will specify the duration and frequency of their use.

Protect the treated areas from excessive sunlight for a few weeks following the procedure to avoid hyperpigmentation or skin damage. Mild bruising, swelling, or discomfort at the injection sites are common side effects and should subside within a few days. Applying ice packs to the affected areas may help alleviate any discomfort or reduce swelling. Dr. Naar may recommend over-the-counter pain relievers to manage any residual discomfort that persists after the procedure. Most patients state the procedure as being painless.

Results

Sclerotherapy results become gradually apparent as the treated blood vessels collapse and are reabsorbed by the body. Multiple treatment sessions may be necessary to achieve desired cosmetic outcomes, depending on the severity and extent of the telangiectasias. While individual experiences may vary, most patients notice a visible reduction in the appearance of spider veins or broken capillaries within two to six weeks following the treatment.

Cost of Spider Vein Treatment in Westlake

During your consultation with Dr. David Naar at Premier Vein Clinic, he will outline the specific details of your treatment plan, including the associated costs. To obtain an accurate estimate tailored to your individual needs, please contact our office at (440) 641-0433 or complete this form for further details.

FAQ

Is Osler-Weber-Rendu Syndrome the same as hereditary hemorrhagic telangiectasia (HHT)?

Yes, Osler-Weber-Rendu Syndrome is another name for HHT.

Is sclerotherapy painful?

The level of discomfort experienced during sclerotherapy is typically minimal and temporary. Most patients report feeling only mild stinging or cramping during the injections. If you have any concerns, discuss them with your medical provider before the procedure.

How many sclerotherapy sessions will I need for spider veins?

The number of sessions required varies from patient to patient and depends on factors such as the severity and extent of the telangiectasias being treated. On average, patients require multiple treatment sessions, scheduled at least four to six weeks apart, to achieve optimal results.

Can I resume normal activities immediately after sclerotherapy treatment?

Yes, most patients can return to their regular activities immediately after sclerotherapy. However, it is advisable to avoid strenuous exercise, hot baths, saunas, or prolonged exposure to sunlight for a few days following the procedure. Your medical provider will provide you with personalized post-treatment instructions to promote a smooth recovery process.

References

  1. Macri A, Wilson AM, Shafaat O, Sharma S. Osler-Weber-Rendu Disease. PubMed. Published 2022. https://www.ncbi.nlm.nih.gov/books/NBK482361/ 
  2. Zarrabeitia R, Concepción Fariñas-Álvarez, Santibáñez M, et al. Quality of life in patients with hereditary haemorrhagic telangiectasia (HHT). Health and quality of life outcomes. 2017;15(1). doi:https://doi.org/10.1186/s12955-017-0586-z